Objective: Atypical teratoid/rhabdoid tumors (ATRT) are rare, aggressive, malignant, central nervous system tumors, most commonly arising from the posterior fossa. Children with ATRT have poor prognoses and low survival rates. There is no established, effective therapy, though most undergo resection and receive chemotherapy and/or radiation therapy. Thus, little remains known regarding the neurocognitive sequelae of pediatric ATRT, particularly from a survivorship standpoint. Method: A case of a now 16-year-old, Hispanic female from a highly populated urban area, diagnosed with left frontal ATRT at four years of age. Initial presentation, neuroimaging, treatment course, and long-term medical and neuropsychological follow-up are described. Commencing four months post-treatment, serial neuropsychological evaluation is presented, along with recent behavioral, emotional, social, and adaptive functioning. Results: Neuropsychological testing reveals left frontal dysfunction, as evidenced by confrontational naming, phonemic fluency, and right-handed fine-motor skill deficits. Additionally, there continues to be evidence of learning disabilities, with frank reading and...

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